Cell Biology | Tay-Sachs, Fabry, Gaucher, Niemann-Pick Disease

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  • Опубликовано: 22 янв 2025

Комментарии • 212

  • @alih6953
    @alih6953 3 года назад +131

    If everyone in the world were like Zach, the world would be heaven! Thank you for making 3 videos in 3 days!

    • @NewtonMD
      @NewtonMD 2 года назад

      But... We can't have good things

    • @Fatima-kq6xg
      @Fatima-kq6xg Год назад

      I agree 🧘🏻‍♀️🤍

  • @arokan327
    @arokan327 3 года назад +45

    I just started study medicine one week ago and already, I do nothing else.
    These videos are probably going to be the reason, I pass my exams properly and going to be a knowledgeable doctor.
    Thank you very much for all you've done and all the videos to come!

  • @GraceAdeniyiOlamijulo
    @GraceAdeniyiOlamijulo 13 часов назад

    This video deserves a million views. Thank you for simplifying LSD.

  • @soco2020
    @soco2020 10 месяцев назад

    I would have never made it through my first year of med school without your help. Thank you for all of the great videos.

  • @biancab2231
    @biancab2231 3 года назад +3

    I clap after each video. Thank you so much for doing this, you're a blessing on this app! Virtual hugs

  • @alih6953
    @alih6953 3 года назад +11

    Zach you are amazing! So close to 900K subs mate! Whenever I see your videos, I am so grateful. 3 Videos in 3 Days . In Soccer you would be Hat Trick Hero. In Basketball you would be MVP

  • @Muhammad.1885
    @Muhammad.1885 3 года назад

    This is the first video I've seen on RUclips without a dislike! Thanks Ninja!

  • @linhyybear143
    @linhyybear143 3 года назад +3

    Making STEP 1 studying so much easier. Thank you so much!

  • @yashwantlonkar7074
    @yashwantlonkar7074 Год назад

    This man is a Angel for medical students.
    Thank you so much.
    Keep it up.

  • @alih6953
    @alih6953 3 года назад +4

    Zach I want to say from the bottom of my heart you represent the best of humanity! You are giving so much and asking for so little. You are an angel mate! (Have tears in my eyes)

  • @cedricwey1621
    @cedricwey1621 Год назад

    Danke!

  • @noorjahanjaganath2582
    @noorjahanjaganath2582 Год назад

    you saved my many hours of reading
    God Bless you Zach

  • @xxacidusxx2
    @xxacidusxx2 3 года назад +3

    I memorized a chart for this section because I didn't understand the purpose of these enzymes in lysosomes. So basically what I think I'm getting from this video is that all the sphingolipidoses are due to defects in lipid metabolism. These lipids are all derivatives of sphingosine and are part of the cell membrane whether they are sphingomylelins, ceramides, cerebrosides, or gangliosides. They are not the same as TG that undergo beta oxidation, they are broken down in lysosomes and are either released in the cytoplasm or ECM via secondary lysosomes. They are used in the liver for LDL degradation, in all cells that undergo autophagocytoses, and in the WBC for pathogen degradation. Fabry is the only XR disease the rest is AR, Fabry and Gaucher usually present in adulthood whereas the other diseases present during childhood. Only gaucher disease may present with increased risk of infection due to pancytopenia, differentiating Tay Sach from Niemann Pick via hyperreflexia vs hyptonia and no hepatosplenomegaly vs hepatosplenomegaly.

  • @zman0894
    @zman0894 2 года назад +3

    I love all of your videos, Zach! So helpful in all my courses I’ve taken thus far and I’m just 2 semesters away from graduating, then onto graduate school 😃 you’ve made learning an enjoyable experience. Do you think you could make a video series of ways that YOU study? Since you clearly have retained so much information 😃 thank you!

  • @alishaakhani1016
    @alishaakhani1016 2 года назад +1

    Such a simple, to the point, awesome video!!! You make learning fun. Keep going

  • @jjjjj2706
    @jjjjj2706 3 года назад +28

    i can't believe this man is actually real!!! a genius indeed

  • @drirfan72941
    @drirfan72941 3 года назад +2

    I will say only one sentence "you are amazing zach"❤️❤️❤️

  • @shelbyschwarz7901
    @shelbyschwarz7901 2 года назад

    I’m a third year phd student at Notre dame working on npc disease. Loved the video, and it was really impressive.

  • @jelenajovanov4149
    @jelenajovanov4149 3 года назад +1

    20 years after biology semester, recapitulation with Zach.Thank you Ninja Nerd🙏

  • @duhaali03
    @duhaali03 Год назад

    This is wonderful. Everything I wanted to know and understand about the lysosome, I found it here. Thank you very much😊

  • @UsmanHayat-h4s
    @UsmanHayat-h4s Месяц назад

    Even I am pre medical students preparing myself for competitive exam still I watch your videos because it's a good resource to make clear concept from them

  • @리뉴얼바디-n5y
    @리뉴얼바디-n5y 3 года назад +3

    Thank you so much
    You make my knowledge concrete!
    I have been studying biology with you.
    I hope you feel our happy 😊
    Be safe from Covid19! Be always happy!

  • @rodneyklinger5811
    @rodneyklinger5811 3 года назад

    Dude, you are a hero! We all love you!
    Thanks to you and your team!

  • @gsudheerreddy1954
    @gsudheerreddy1954 3 года назад

    Congrats zach bro you are near to 1million

  • @ayeshashabbir2324
    @ayeshashabbir2324 3 года назад +13

    Please make video on some tips for studying and How to make effective notes and how to keep maintain focus.. I know there is a lot on videos on RUclips but you are deep explainer so it will be helpful.. Thanks in advance 😇

    • @granola1998
      @granola1998 3 года назад +1

      Yessss please 🙏🙏

    • @drirfan72941
      @drirfan72941 3 года назад +2

      Best thing is to make notes form videos lecture or you can do another thing you can also make notes form the different books material and also from google and makes different diagram and writes in your own words as it will be easy for your revision.

    • @granola1998
      @granola1998 3 года назад +1

      @@drirfan72941 thanks you! 😊❤️

    • @alih6953
      @alih6953 3 года назад

      he already did a studying video on his channel 2-3 weeks ago

  • @nyananguei1928
    @nyananguei1928 3 года назад

    Thanks you ninja nerd for the best you have done.

  • @ramonfontes9025
    @ramonfontes9025 3 года назад +1

    U are just AMAZING Professor !

  • @thokomasango2294
    @thokomasango2294 Год назад

    Thank you for making it easy for me to understand 🙏🏾💞

  • @김영미-y8e1j
    @김영미-y8e1j 3 года назад

    The best lecture I've ever seen! Thank you so much!

  • @Dr.Number01
    @Dr.Number01 Год назад

    stunning!! Love all the lectures. Bless you all.

  • @amalsingha1894
    @amalsingha1894 Год назад

    You make the lesson very easy.

  • @antoniogomez-rguez1038
    @antoniogomez-rguez1038 2 года назад

    OMG you are simply amazing, i enjoyed the full lecture. Thank you very much for this!

  • @janislechner3523
    @janislechner3523 2 года назад

    you are so awesome to watch!! Thank you for making and sharing your super personality with us!! love ur videos!!

  • @pushpashakya3051
    @pushpashakya3051 2 года назад +1

    Thank you so much for this knowledge🙂

  • @aloksanidhya6476
    @aloksanidhya6476 3 года назад

    Loves your teaching style...❤️❤️🙏🙏

  • @albuanastasya
    @albuanastasya 3 года назад

    Loved it! Thank you, Zach, appreciate your contribution!

  • @megha111
    @megha111 8 месяцев назад

    Thank you so much for this wonderful video❤

  • @user-tp7xc9fz9c
    @user-tp7xc9fz9c 2 года назад

    You are a good teacher, thank you.

  • @thirmizidiallo6729
    @thirmizidiallo6729 Год назад

    can never thank you enough for this !

  • @God_King6
    @God_King6 2 года назад

    Best up and coming rapper!!!

  • @Mari-qo4dh
    @Mari-qo4dh 3 года назад

    great video! I like you explained end to end process

  • @vernelloydcalunsag3763
    @vernelloydcalunsag3763 3 года назад

    Thank you for making this video.. you make things simplier.

  • @Zetsuke4
    @Zetsuke4 3 года назад

    can’t wait to watch this!

  • @franzcalipusan3367
    @franzcalipusan3367 Год назад

    This helped a lot sir.... Thank you so much...

  • @salaheddinehouache1015
    @salaheddinehouache1015 3 года назад

    Great as usual... good job !

  • @gargsiblings6230
    @gargsiblings6230 3 года назад

    Thank you so much for being just the way u r

  • @akhtarparas3238
    @akhtarparas3238 3 года назад

    Amazing sir keep making videos on cell biology lots of love from Pakistan ❤❤

  • @dmbms
    @dmbms 3 месяца назад

    Thank you so much.
    Keep it up.

  • @basharalzohily7017
    @basharalzohily7017 2 года назад

    Many thanks. It was really helpful.

  • @idrissayusuf6561
    @idrissayusuf6561 3 года назад

    Amazing explanation as always

  • @claudiaciciotti9973
    @claudiaciciotti9973 3 года назад

    Great video!! As always

  • @williamowen7152
    @williamowen7152 Год назад

    Don't often see anything on LSDs like this. Thanks for raising the profile. Woild like to see something on lysosomal membrane proteins especially NPC1 (Niemann-Pick 1 protein. Amazing small writing!

  • @mohammadnawaz4450
    @mohammadnawaz4450 2 года назад +1

    Brilliant video

  • @bobwilliams2679
    @bobwilliams2679 3 года назад +1

    I’m currently taking a paramedic class thank you for your videos. Tremendous help!
    For a future video topic can you do a video on med math . We were learning about IV piggybacks with dopamine drips of different Concentrations. Some of your clear explanation would really be helpful!

  • @jelwzhoodgirl6169
    @jelwzhoodgirl6169 2 года назад

    I love how you are repeating facts with having these little breaks, so one has a change to suggest frist

  • @abdisamadahmedyasinshcali8927
    @abdisamadahmedyasinshcali8927 3 года назад

    only 100k away from the million lets do this ninja nerds!

  • @gsudheerreddy1954
    @gsudheerreddy1954 3 года назад

    Thank you zach bro!! 😊

  • @titusnelson1024
    @titusnelson1024 3 года назад

    As an old engineer I had a brain freeze about 1:00 in. Then about 10:00 when you talk about Receptor Mediated Endocytosis a few brain cells came out of hibernation connecting stress analysis and vibrations and I nearly had a stroke. I couldn’t even relate to nonlinear optics. Holey-Moley I guess I better start with basic biology. However, after a third go of it some synapses are forming.

  • @alfredovictoriagonzalez7462
    @alfredovictoriagonzalez7462 3 года назад

    YOU ALL ROCK THANK YOU

  • @rusudankurua6705
    @rusudankurua6705 3 года назад

    Thank you Zach

  • @naveenajyothi1244
    @naveenajyothi1244 3 года назад

    Wow extraordinary it's makes me feel better understanding thankyou so much sir

  • @ikka5314
    @ikka5314 Год назад

    Thank you for this amazing video

  • @arizonablossom8635
    @arizonablossom8635 3 года назад

    Thanks a lot for your hard work👍🙏

  • @aind1272
    @aind1272 3 года назад

    bro your energy while explaining is different!

  • @abdussamad644
    @abdussamad644 3 года назад

    Thank you sir for making amazing lactures

  • @MEZ4RCI
    @MEZ4RCI 3 года назад

    it was an awesome lecture but I wished that you explained other sphingolipidoses. like krabbe farber etc. still was a nice roundup video. loved it.

  • @ferricyanide8112
    @ferricyanide8112 3 года назад

    Thank you, Sensei

  • @vijaypallipamu4890
    @vijaypallipamu4890 4 месяца назад

    Hi fantastic lecture I can’t believe it

  • @abdussamad644
    @abdussamad644 3 года назад

    Sir also deliver lectures on remaining cytology such as details description on nucleus . Cell membrane. And so on👍👍👍👍👍👍👍

  • @dorcasb2194
    @dorcasb2194 3 года назад

    Kindly do a video series on how to read and interpret X-rays and other radiographs. Thanks

  • @yusufali5812
    @yusufali5812 3 года назад

    Excellent Lecture! Please provide me with the links for all of your biochemistry and molecular biology lectures

  • @abirmohammadkhan6742
    @abirmohammadkhan6742 3 года назад

    You are amazing...Love your videos...

  • @sunilmoktan838
    @sunilmoktan838 Месяц назад

    Superb❤❤❤

  • @UsmanHayat-h4s
    @UsmanHayat-h4s Месяц назад

    After taking you lectures I am enable for asking any type questions to someone

  • @abdelgadireshaq3990
    @abdelgadireshaq3990 3 года назад

    I'm always waiting for your vedio guys 🌸

  • @shabihusain3901
    @shabihusain3901 3 года назад

    His liiitttlle bit deeper is very deep😌

  • @hosaymamozay8773
    @hosaymamozay8773 Год назад

    You are a blessing

  • @anushyabeulah2854
    @anushyabeulah2854 3 года назад

    Very good explanation..

  • @niyadeo7970
    @niyadeo7970 Год назад

    Amazing!

  • @mnhlhmo7967
    @mnhlhmo7967 3 года назад

    thanks Zach

  • @aliamer2868
    @aliamer2868 3 года назад

    Thanks again and again

  • @lilouvincent8407
    @lilouvincent8407 2 года назад

    Je parle pas anglais et j'ai quand même trouver son cours super

  • @roro13chavez74
    @roro13chavez74 3 года назад

    Wey neta que te amo, explicas super bien todo

  • @guna7558
    @guna7558 3 года назад

    Really,u r awesome n your videos r also awesome n very much helpful....thank you so much zach....lots of love (India)😍😍😍....please upload videos of all the cell organelles🙏

  • @heydazzling
    @heydazzling 2 года назад

    thank you so much !!

  • @yasirmohammedali
    @yasirmohammedali 3 года назад

    Hi ... Thanks a lot for the videos

  • @khalil_4924
    @khalil_4924 3 года назад +1

    Wow Zach you are explaining stuff that we used to think that they are non-doable in medschool and never understand 😂 lysosomal storage diseases are 💀💀

  • @karthikarumugam1512
    @karthikarumugam1512 3 года назад

    Sir pls post more videos on pathology , pharmacology and microbiology....
    We r waiting....🙏🙏❤️

  • @EllenSweden
    @EllenSweden 2 года назад

    Hi Zach,
    Thank you so much for the amazing explanation, I have a question to share with you regarding the NPC disease (Niemann pick type c)!
    Out of this explanation, what is the possible consequences of following a low carb & high fat diet and Intermittent fasting on NPC cells
    and how consuming different kind of fat can increase or slow down the process of the disease in the cell level?

  • @johnh6093
    @johnh6093 3 года назад

    Thank you so much

  • @luancarvalho1250
    @luancarvalho1250 3 года назад +1

    god damn i love you guys so, so, so much

  • @atulsinghtech52
    @atulsinghtech52 2 года назад

    Very nice content.

  • @kferdous5994
    @kferdous5994 3 года назад

    We want more video on organells of cell I mean on ribosome on golgi aperatus etc

  • @SandeepKumar-yp2ke
    @SandeepKumar-yp2ke 3 года назад

    Awesome 👌

  • @wajahatabbasi5673
    @wajahatabbasi5673 3 года назад

    Sir I am ur biggest fan sir 😌💓

  • @peacefromtheashesofwar4181
    @peacefromtheashesofwar4181 3 года назад +2

    I hope you be successful in your entire life and you worth it for all your dedication and your perseverance. I know you're work is not so easy but it worth.

  • @sudhirgairola4889
    @sudhirgairola4889 2 года назад

    Nice information

  • @earnwithbasam5541
    @earnwithbasam5541 2 года назад

    Excellent informative vedio

  • @abdelgadireshaq3990
    @abdelgadireshaq3990 3 года назад

    Wow❤️
    Very nice

  • @skiteflies3
    @skiteflies3 2 года назад

    Thank you so much for the video, such a clear concise explanation. However, does anyone know why Tay Sachs and Nieman Picks present so similarly besides the hepatomegaly while Gaucher and Fabry dont. Also why does gaucher seem to affect the bone (is it because the enzyme that its deficient in is only found in that bone?)? What is the reason behind Fabry causing Angiokeratomas while the others are less likely? These might all be moot points, but Im just curious to know if there is an actual answer or if its just by experience that these are the most common presentations?